Cytochrome c oxidase assembly protein pet191

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August undefined, 2024

http://pfam-legacy.xfam.org/family/Pet191_N WebDescription. Cytochrome c oxidase deficiency is a genetic condition that can affect several parts of the body, including the muscles used for movement ( skeletal muscles ), the heart, the brain, or the liver. Signs and symptoms of cytochrome c oxidase deficiency usually begin before age 2 but can appear later in mildly affected individuals.

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WebJul 19, 2005 · Essential for the assembly of the mitochondrial respiratory chain complex IV (CIV), also known as cytochrome c oxidase (PubMed:23125284). Acts as a chaperone in the early steps of cytochrome c oxidase subunit II (MT-CO2/COX2) maturation, stabilizing the newly synthesized protein and presenting it to metallochaperones SCO1/2 which in … WebJan 1, 2024 · This study identified a copper binding P-type ATPase, multicopper oxidase, cytochrome c oxidase subunits 1 and 2 (Cox1 and Cox2) as well as seven copper chaperones, including cytochrome c oxidase assembly protein 11 (Cox11), Cox17, Cox19, PET191, Sco1 and Sco2 and the Cmc1-like cytochrome c oxidase biogenesis … funny girl broadway twitter

Sequence and chromosomal localization of two - Springer

WebApr 8, 2011 · The C2orf64 protein contains two Cx 9 C motifs that are highly conserved among all eukaryotes with complex IV (Figure 4A). ... Pet191 is a cytochrome c oxidase assembly factor in Saccharomyces cerevisiae. Eukaryot. Cell, 7 (2008), pp. 1427-1431. View Record in Scopus Google Scholar. 20. WebThe nuclear genes PET117 and PET191 are required for the assembly of active cytochrome c oxidase in S. cerevisiae, yet their gene products are not subunits of the … WebOct 16, 2009 · Abstract. Mutations in SCO2, a protein required for the proper assembly and functioning of cytochrome c oxidase (COX; complex IV of the mitochondrial respiratory chain), cause a fatal infantile cardioencephalomyopathy with COX deficiency. We have generated mice harboring a Sco2 knock-out (KO) allele and a Sco2 knock-in (KI) allele … funny girl cast album beanie

Pet191 Is a Cytochrome c Oxidase Assembly Factor in …

Cytochrome c oxidase assembly protein pet191

WebJan 22, 2024 · Primary Citation of Related Structures: 5Z62. PubMed Abstract: Respiration is one of the most basic features of living organisms, and the electron transport chain complexes are probably the most complicated protein system in mitochondria. Complex-IV is the terminal enzyme of the electron transport chain, existing either as randomly … WebSep 30, 2024 · Abstract. Cytochrome c oxidase is the terminal complex of eukaryotic oxidative phosphorylation in mitochondria. This process couples the reduction of electron carriers during metabolism to the reduction of molecular oxygen to water and translocation of protons from the internal mitochondrial matrix to the inter-membrane space.

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WebThe presence of a twin Cx 9 C sequence motif does not ensure that import is MIA-mediated, since the CcO assembly protein Pet191 has a twin Cx 9 C motifs and is imported in a Mia40- independent ... WebPet191 is a cytochrome c oxidase assembly factor in Saccharomyces cerevisiae The twin-Cx(9)C motif protein Pet191 is essential for cytochrome c oxidase maturation. …

WebInvolved in the assembly of cytochrome c oxidase. Features Showing features for domain, motif. Expand table GO Annotations Expand table Complete GO annotation on QuickGO … WebComplex IV, or cytochrome c oxidase (COX), is the terminal enzyme of the mitochondrial respiratory chain that catalyzes oxidation of cytochrome c by molecular oxygen. The …

WebGene ID: 5077169, updated on 8-Aug-2024. Summary Other designations. cytochrome c oxidase assembly protein (Pet191), putative WebJun 1, 2012 · 1.More than 50 years of eukaryotic cytochrome c oxidase assembly. Mitochondrial cytochrome c oxidase (COX) is a multimeric copper-heme A terminal oxidase that functions as an electron-driven proton pump and plays fundamental roles in eukaryotic cell respiration and aerobic energy production. COX catalyzes the transfer of …

WebThe role of cytochrome c is to carry electrons from one complex of integral membrane proteins of the inner mitochondrial membrane to another (Fig. 10.3). The electron donor is cytochrome c-1. The electron acceptor is cytochrome c oxidase. Both of these integral membrane proteins have binding sites for the peripheral membrane protein cytochrome c.

WebJun 1, 2008 · The twin-Cx9C motif protein Pet191 is essential for cytochrome c oxidase maturation. The motif Cys residues are functionally important and appear to be present … gis rush county indianaWebSep 30, 2024 · Cytochrome c oxidase and most oxidative phosphorylation complexes are the product of the nuclear and mitochondrial genomes. This poses a series of topological … funny girl broadway window cardWebProtein required for assembly of cytochrome c oxidase; exists as an oligomer; described as both an integral mitochondrial inner membrane protein facing the intermembrane … gis rusk countyWebMay 23, 2008 · Europe PMC is an archive of life sciences journal literature. gis rutherford co ncWebSep 13, 2005 · Function. Required for the transduction of an SCO1-dependent redox signal from the mitochondrion to ATP7A to regulate cellular copper homeostasis ( PubMed: 23345593 ). May be required for the assembly of mitochondrial cytochrome c oxidase ( By similarity ). By similarity. gis rubricWebC motif protein Pet191 is essential for cytochrome c oxidase maturation. The motif Cys residues are functionally important and appear to be present in disulﬁde linkages within … funny girl broadway tourWebFunction Required for the assembly of yeast cytochrome oxidase. Involved in the biosynthesis of heme A and the initial step in this pathway, the hydroxylation of heme O, … funny girl cast broadway revival